Data for: SPINK1 and pancreaticobiliary maljunction: An unusual co-etiology of pancreatitis

Published: 31 December 2019| Version 1 | DOI: 10.17632/m9yrsnyptz.1
Piyawan Chiengkriwate,
Surasak Sangkhathat,
Kulpreeya Sirichamratsakul,
Wison Laochareonsuk


Chronic pancreatitis (CP) in childhood is a rare condition and its etiology varies with mainly associated with genetic abnormalities, autoimmune pancreatitis, and obstruction. The authors describe a 6-year-old girl presented with abdominal pain and diagnosed as CP with an infected peripancreatic fluid collections (peri-PFC), and found a pancreaticobiliary maljunction (PBM) together with a SPINK 1 mutation at N34S codon. This combination of an anatomical obstruction and genetic mutation should be aware, in early childhood presented with pancreatitis.